Cochlear Implants - Science topic

Background/Objectives: Early pediatric cochlear implantation positively impacts early language outcomes. The Teenager and Young Adults Cochlear Implant (TAYACI) study investigates the long-term outcomes of early implantation and factors influencing variability among cochlear implant (CI) users. This article outlines participants’ background, early...

Reticular dysgenesis (RD) is a rare inborn error of immune cell formation defined by severe combined immunodeficiency, agranulocytosis and sensorineural deafness. We report a case of successful haploidentical maternal hematopoietic stem cell transplantation (HSCT) in a boy with RD detected by TREC newborn screening. The patient was admitted to our...

Chronic otitis media (COM) is treated medically and/or surgically. Ossiculoplasty for COM with severe-to-profound hearing loss has not been recommended because the severity of hearing loss before surgery is negatively associated with postoperative hearing improvement. Our study assessed the effectiveness of ossiculoplasty for severe-to-profound hea...

Purpose The breadth of binaural pitch fusion, the integration of sounds differing in frequency across the two ears, can limit the ability to segregate and understand speech in background noise. Binaural pitch fusion is one type of central auditory processing that may still be developing in the pre-adolescent age range. In addition, children with he...

Objective Identify MRI‐related cochlear implant (CI) adverse events from the Food and Drug Administration (FDA) Manufacturer and User Facility Device Experience (MAUDE) database and determine whether devices with diametric magnets are associated with reduced adverse events. Methods Data on MRI‐related adverse events were collected from the MAUDE d...

We surveyed to explore how Japanese cochlear implant users perceive and enjoy music, as well as factors related to their music enjoyment. The survey gathered responses from 102 participants, showing that many continue to enjoy music after getting the implant and are keen on enjoying it even more. A time series analysis revealed that enjoyment of mu...

Cochlear implants (CIs) are surgically implanted hearing devices, which allow to restore a sense of hearing in people suffering from profound hearing loss. Wireless streaming of audio from external devices to CI signal processors has become common place. Specialized compression based on the stimulation patterns of a CI by deep recurrent autoencoder...

Cochlear implants (CIs) are neural prostheses that restore some level of hearing capacity, albeitconveying a less fine-grained speech signal than normal hearing conditions. For example, CIsconvey altered fundamental frequency (F0) information, disrupting the perception of lexical stress(e.g., distinguishing between the noun CONtent and the adjectiv...

Background/Objectives: Cochlear implantation (CI) is a transformative intervention for individuals with sensorineural hearing loss, providing auditory and speech perception improvements. Traditional CI activation occurs 4–6 weeks post-surgery; however, recent advancements allow for early activation within 1–2 days. The integration of data logging i...

Resumo A família é fundamental no desenvolvimento de crianças com Deficiência Auditiva e Transtorno do Espectro Autista simultâneos, usuárias de Implante Coclear, possibilitando o desenvolvimento de Habilidades Sociais, relacionadas às Habilidades Sociais Educativas dos cuidadores e, redução de problemas de comportamento. Este estudo objetivou desc...

Purpose To assess whether increasing experience with implantation of a thin preformed electrode array for perimodiolar insertion reduces the incidence of tip fold-over (TFO). Methods The retrospective study included 100 patients who received a cochlear implant (CI) with the Slim Modiolar (SM) electrode array (Cochlear, Sydney, Australia) at a univ...

Cochlear implants improve auditory function in individuals with severe hearing loss, yet cochlear implant users often struggle with tasks such as identifying speaker characteristics and musical elements. While music therapy shows promise in addressing these deficits, standardized rehabilitation protocols, especially those focusing on music-based so...

Introduction Penetrating middle ear trauma-induced pneumolabyrinth is an exceedingly rare finding in pediatric patients. This condition can lead to significant hearing and vestibular dysfunction. We present two pediatric cases, highlighting their clinical complexity. Cases presentation Case 1 presented a 9-year-old boy with hearing loss, vertigo,...

Etiological factors affecting outcomes of cochlear implants (Cis) are known; however, a direct comparison of efficacy based on lesion location is needed. We aimed to systematically examine the current evidence to compare the effectiveness of CIs in patients with presynaptic versus postsynaptic neuropathy.

Background: Etiological factors affecting outcomes of cochlear implants (Cis) are known; however, a direct comparison of efficacy based on lesion location is needed. We aimed to systematically examine the current evidence to compare the effectiveness of CIs in patients with presynaptic versus postsynaptic neuropathy. Methods: A comprehensive litera...

Introducción: las personas con desorden del espectro de neuropatía auditiva tienen problemas en el procesamiento del sonido y la comprensión del lenguaje, por tener una o varias estructuras de la vía auditiva afectadas. Se ha planteado como opción de rehabilitación el implante coclear. La electrococleografía aplicada en pacientes con desorden del e...

Introduction: Transimpedance matrix measurement (TIM) is an electrophysiological measurement protocol of the impedance patterns of electrode contacts within the cochlea. Several studies have reported that TIM is an effective tool for the identification of abnormal electrode array placement. However, the normative values for properly inserted electr...

Purpose Prelingual deaf children with cochlear implants show lower digit span test scores compared to normal-hearing peers, suggesting a working memory impairment. To pinpoint more precisely the subprocesses responsible for this impairment, we designed a sequence reproduction task with varying length (two to six stimuli), modality (auditory or visu...

Objectives Typically developing children (TD) exhibit linguistic outcomes commensurate with their chronological age, as linguistic input critically shapes early language development. Conversely, children with sensory deficits, such as hearing loss (HL), lack access to the auditory-linguistic information essential for developing spoken language. Thi...

Cochlear implants (CIs) are devices that restore the sense of hearing in people with severe sensorineural hearing loss. An electrode array inserted in the cochlea bypasses the natural transducer mechanism that transforms mechanical sound waves into neural activity by artificially stimulating the auditory nerve fibers with electrical pulses. The per...

Bimodal stimulation, combining cochlear implant (CI) and acoustic input from the opposite ear, typically enhances speech perception but varies due to factors like temporal mismatch. Previously, we used cortical auditory evoked potentials (CAEPs) to estimate this mismatch based on N1 latency differences. This study expands on that by assessing the i...

Cochlear implants (CIs) restore the perception of sound for individuals with severe to profound hearing loss by employing electrical stimulation to directly activate the remaining auditory neurons. Post-implantation ipsilateral hearing loss has been observed in every patient series involving hearing preservation cochlear implantation. Patients with...

Using the syntactic priming paradigm, this study investigated abstract syntactic knowledge of Chinese transitive structures (i.e., subject-verb-object [SVO], BA, and BEI) in deaf children with cochlear implants (CIs). Specifically, we focused on the differences in the development of various syntactic structures (within CI children and compared with...

A COCHLEAR IMPLANT (CI) IS an electronic device that is surgically implanted to re-store hearing in individuals with severe to profound sensorineural hearing loss. Due to the technological limitations of these devices, a distorted spectral detail of the sound and a reduced dynamic range is transmitted to the auditory system, which in turn severely...

Abstract The aim of the study was to assess the functional outcome of children who underwent Auditory verbal therapy followed by cochlear implantation using The Parents’ views and experiences with pediatric cochlear implant questionnaire (PVECIQ). Hearing impaired children who have completed minimum of 5 years of auditory verbal training (AVT) afte...

Introduction Adults with cochlear implants (CIs) need periodic programming of their speech processors to take advantage of alternative adjustments. However, this requires patients to attend the CI center in person. Objectives To evaluate the feasibility of speech processor (SP) self-programming with remote assistance in CI users. To establish the c...

Background Cochlear implants (CI) with off-the-ear (OTE) and behind-the-ear (BTE) speech processors differ in user experience and audiological performance, impacting speech perception, comfort, and satisfaction. Objectives This systematic review explores audiological outcomes (speech perception in quiet and noise) and non-audiological factors (dev...

Background/Objectives: The cortical auditory evoked potential P1 response is a biomarker of cortical auditory maturation for tracking longitudinal cortical maturation in children with hearing loss after treatment with hearing aids and/or cochlear implants. In conjunction with hearing treatments, children with hearing loss commonly receive language...

Ritva Torpan psykologian väitöskirja ”Pitch-related auditory skills in children with cochlear implants: The role of auditory working memory, attention and music” tarkastettiin Helsingin yliopistossa 6.11.2015. Vastaväittäjänä toimi Dr., Res. Dir. Curtis Ponton, PhD (House Research Institute ja Compumedics Neuroscan, Yhdysvallat) ja kustoksena profe...

Background and purpose To evaluate various anatomical parameters and their relationship to chorda tympani nerve (CTN) injury and round window (RW) access during cochlear implantation. Materials and methods Ultra-high-resolution CT images of 66 patients were retrospectively reviewed and compared with operative reports. The facial recess and the rou...

Purpose Children develop social-pragmatic understanding with the help of sensory, cognitive, and linguistic functions by interacting with other people. This study aimed to explore (a) associations between auditory, demographic, cognitive, and linguistic factors and social-pragmatic understanding in children who use bilateral hearing aids (BiHAs) or...

Objectives: The aims of this study were to compare pre- and post-operative word recognition scores (WRSs) for the adult Spanish-speaking population and to describe their cochlear implant (CI) performance trajectory. Methods: A retrospective chart review (n = 115) was completed for Spanish-speaking post-lingually deafened adults who underwent a trad...

Speech separation approaches for single-channel, dry speech mixtures have significantly improved. However, real-world spatial and reverberant acoustic environments remain challenging, limiting the effectiveness of these approaches for assistive hearing devices like cochlear implants (CIs). To address this, we quantify the impact of real-world acous...

Cochlear implantation (CI) is a highly effective treatment for profound hearing loss in elderly individuals, including those with ARHL. However, factors influencing the success of CI in the elderly population are not fully understood. Hence, we sought to investigate the association of regional cerebellar gray matter volume with effectiveness of CI...

Background/Objectives: Ichthyosis refers to a group of genetic disorders characterized by extensive scaling of the skin. Syndromic ichthyosis, such as KID syndrome, is associated with mutations in connexin 26, resulting in a triad of keratosis, ichthyosis, and deafness. Cochlear implant (CI) is considered an effective rehabilitation option for seve...

Introduction The Nijmegen cochlear implant questionnaire (NCIQ) is a quantifiable self-assessment health-related quality of life (HRQoL) tool used internationally to determine quality of life (QoL) in cochlear implant (CI) users and to evaluate the implant's subjective benefits. Objective This study aimed to validate the Danish version of the quest...

Deafness, dystonia, and central hypomyelination (DDCH) syndrome (OMIM #300475) is a rare X-linked genetic disorder characterized by developmental delays, deafness, central hypomyelination, and dystonia. We report the first Korean familial case involving twin boy and girl carrying a novel pathogenic BCAP31 variant which was inherited from their moth...

Background Hybrid coronary revascularisation benefits patients with multivessel disease, as it amalgamates the minimally invasive direct coronary artery bypass (MIDCAB) procedure and percutaneous coronary intervention (PCI). Case summary We present a 63-year-old female with triple-vessel coronary artery disease including marked ostial stenosis of...

Aim: The aim of this study was to assess the subjective experiences of adults with different cochlear implant (CI) configurations—unilateral cochlear implant (UCI), bilateral cochlear implant (BCI), and bimodal stimulation (BM)—focusing on their perception of speech in quiet and noisy environments, music, environmental sounds, people’s voices and t...

Cochlear implants are well established devices for treating severe hearing loss. However, due to the trauma caused by the insertion of the electrode and the subsequent formation of connective tissue, their clinical effectiveness varies. The aim of the current study was to achieve a long-term reduction in connective tissue growth and impedance by co...

Purpose Evaluate the feasibility and safety of a robotic electrode insertion in pediatric cochlear implantation and compare the results with manually inserted electrodes in the same subject. Methods Retrospective case series review of four children who underwent bilateral cochlear implantation with the same array: on one side, the array was insert...

When listening to speech under adverse conditions, listeners compensate using neurocognitive resources. A clinically relevant form of adverse listening is listening through a cochlear implant (CI), which provides a spectrally degraded signal. CI listening is often simulated through noise-vocoding. This study investigated the neurocognitive mechanis...

During cochlear implant (CI) surgery, it is desirable to perform intraoperative measurements such as Electrocochleography (ECochG) to monitor the inner ear function and thereby to support the preservation of residual hearing. However, a significant challenge arises as the recording location of intracochlear ECochG via the CI electrode changes durin...

The article examines the socio-educational barriers and facilitators faced by families of children with cochlear implants (CI) in Andalucía (a region in southern Spain). Through a qualitative approach based on surveys and interviews, three main categories of limitations are identified: access to and quality of services, parental stress related to c...

Background: Parental satisfaction is an important factor in the evaluation of early intervention programs but is rarely investigated. The Muenster Parental Program (MPP) is a short, evidence-based early intervention program that focuses on parental responsiveness. It is a family-centered intervention for parents of infants aged 3–18 months who have...

Background/Objectives: This study aims to evaluate factors influencing revision cochlear implant surgeries, including patient demographics, surgical techniques, and radiological findings. The main aim was to identify factors influencing surgical success to inform clinical treatment and enhance patient outcomes. Methods: This cross-sectional study i...

Predicting cochlear implant performance: Moving beyond single biomarkers and leveraging artificial intelligence Matthew Shew, Amit Walia, and Craig A. Buchman highlight that the significant variability in speech perception among cochlear implant users can be addressed by using a multi- faceted approach that incorporates emerging technologies like m...

Tinnitus, a widespread condition affecting numerous individuals worldwide, remains a significant challenge due to limited effective therapeutic interventions. Intriguingly, patients using cochlear implants (CIs) have reported significant relief from tinnitus symptoms, although the underlying mechanisms remain unclear and intracochlear implantation...

Peripheral hearing loss is associated with the cross-modal reorganization of the auditory cortex, which can occur in both pre-and post-lingual deaf cases. Back-ground/Objectives: Whether to rely on the visual cues in cases with severe hearing loss with adequate amplification is a matter of debate. So, this study aims to study visual evoked potentia...

Hearing loss is an impairment that affects a large population worldwide. Cochlear implant (CI) surgery is an effective solution, especially in patients with residual, natural hearing. However, the risk of intracochlear damage during CI surgery, which impairs residual hearing, remains as a concern. It has been shown that intra-operative monitoring (...

Digits-in-Noise (DIN) tests have been widely applied to assess hearing function and speech-in-noise perception, but their robustness to variations in digit stimuli between listener groups remains unknown. We developed a DIN test for research and clinical applications and evaluated it across different listener groups, including users of cochlear imp...

Background The elderly population is particularly susceptible to the development of age‐related hearing loss and cognitive impairment. The gradual decline in auditory perception often goes unnoticed, leading to a detrimental impact on their quality of life, mental well‐being, and overall communication skills. Extensive research indicates that prolo...

This comprehensive review explores the implications of artificial intelligence (AI) in addressing cochlear implant (CI) issues and revolutionizing the landscape of auditory prosthetics. It begins with an overview of ear anatomy and hearing loss, then explores a review of CI technology and its current challenges. The review emphasizes how advanced A...

Purpose The aim of this study was to measure the effects of frequency spacing (i.e., F2 minus F1) on spectral integration for vowel perception in simulated bilateral electric–acoustic stimulation (BiEAS), electric–acoustic stimulation (EAS), and bimodal hearing. Method Twenty listeners with typical hearing participated in synthetic vowel recogniti...

Zusammenfassung Heute ist die Versorgung hochgradig Schwerhöriger und ertaubter Patienten mit einem Cochlea-Implantat Routine. Allein an der Medizinischen Hochschule in Hannover werden pro Jahr mehr als 500 Patienten mit einem Cochlea-Implantat (CI) versorgt, d. h. der Patienten-Pool der CI-versorgenden Zentren steigt jedes Jahr signifikant. Weltwe...

Objectives This study aimed to examine factors that influence postoperative rehabilitation outcomes in children with cochlear implants, using a knowledge–attitude–practice (KAP) framework. Design A total of 683 children with cochlear implants participated in this study. Hearing and speech assessments were conducted through face-to-face and/or tele...

Los niños con pérdida auditiva (PA) portadores de implantes cocleares pueden mostrar dificultades en las habilidades de función ejecutiva (FE), pero se desconoce si estas limitaciones están presentes en niños con menor grado de PA portadores de audífonos. Este estudio tiene por objetivos evaluar cómo afecta el grado de PA a la FE e identificar qué...

Background Cochlear implants (CIs) are neuroprosthetic devices which restore hearing in severe-to-profound hearing loss through electrical stimulation of the auditory nerve. Current CIs use an externally worn audio processor. A long-term goal in the field has been to develop a device in which all components are contained within a single implant. He...

Purpose Unilateral cochlear implant (CI) recipients with limited hearing in the contralateral ear are deprived of the advantages of binaural hearing. To address speech recognition challenges arising from the head shadow effect, a contralateral routing of signal (CROS) device can be used; however, less is known of the broader impact of a CROS device...

Purpose This study aimed to assess the magnitude and direction of dual-task interference in a listening effort dual-task paradigm in individuals with severe-to-profound hearing loss before and in the short- and long-term after cochlear implantation. Design The study sample consisted of 26 adult candidates for cochlear implantation with severe-to-p...

Background Electrically evoked compound action potential (ECAP) can be used to measure the auditory nerve’s response to electrical stimulation in cochlear implant (CI) users. In the Nurotron CI system, extracting the ECAP waveform from the stimulus artifact is time-consuming. Method We developed a new paradigm (“FastCAP”) for use with Nurotron CI...

Background/Objectives: A heterozygous mutation in the WFS1 gene is responsible for autosomal dominant non-syndromic hearing loss (DFNA6/14/38) and Wolfram-like syndrome, which is characterized by bilateral sensorineural hearing loss with optic atrophy and/or diabetes mellitus. However, detailed clinical features for the patients with the heterozygo...