Article

[Bilateral testicular epidermoid cyst in a pediatric patient with Klinefelter syndrome].

Servicio de Urología Infantil, Hospital Universitario La Fe. Valencia.
Actas urologicas españolas (Impact Factor: 1.02). 11/2003; 27(9):742-4.
Source: PubMed

ABSTRACT

Epidermoid cysts of the testis are rare in children (3% of all the testicular tumors). Bilateral appearance has only been described in the pediatric age in 2 cases and none associated to Klinefelter's syndrome. We present, for our knowledge, the first case of bilateral epidermoid testicular cyst associated to klinefelter's syndrome in a boy, highlighting its management and therapeutic approach. We analyze the different kinds of treatment.

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    No preview · Article · Aug 2009 · Chirurgische Praxis
  • [Show abstract] [Hide abstract]
    ABSTRACT: In general teratomas of infants and children carry a malignant potential. Treatment of malignant germ cell tumors occurs in risk adapted multicentric and prospective trials (German Cooperative Protocols Malignant Germ Cell Tumors, MAKEI, and Testicular Tumors, MAHO). The goals of surgical management are complete tumor resection, accurate staging, and preservation of reproductive capability as well as hormonal function. Incomplete resection and immaturity or malignancy within teratomas predisposes to malignant relapses. Congenital orofacial and neck teratomas may compress the airways and lead to specific perinatal problems. Large sacrococcygeal tumors carry a risk of pre- and perinatal death due to cardiac failure and peripartal laceration of large teratomas as well - an interdisciplinary perinatal team is required for these babies. Mediastinal and retroperitoneal teratomas were treated by surgical excision and may require further postoperative chemotherapy. The use of thoracoscopic and laparoscopic approaches is more and more attractive for resection of germ cell tumors. Gonad preserving resections in ovarian or testicular tumors carry specific oncological risks. They are reserved for selected cases. A long term follow-up of patients with germ cell tumors is strongly recommended.
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    ABSTRACT: Testicular epidermoid cyst is a rare benign tumor in children. Although this entity is widely described in adults in literature, there are no large series describing the pathological and radiological findings in children. Knowledge of the sonographic features seen in children may alter surgical treatment. To describe the specific US characteristics of testicular epidermoid cyst in children and to correlate these findings with pathology. All children with pathologically proven epidermoid cyst and preoperative sonograms diagnosed at a single children's hospital between 1978 and 2008 were included. For each child, the medical records, preoperative US and pathological specimens were reviewed and correlated. Eleven patients (ages 1-17 years old) met our criteria. Nine cysts had characteristic target or onion ring appearances, the youngest patient had a simple cyst-like lesion, one cyst had a heterogeneous appearance, and more than 80% of the cysts presented daughter cysts attached along the periphery of the main cyst. In addition to the commonly described findings of the epidermoid cyst (the target and onion ring appearances), simple cysts and the presence of daughter lesions are newly described findings that point to the diagnosis of this benign entity in children.
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