A Sporadic Abdominal Desmoid Tumour Case Presenting with Intermittent Intestinal Obstruction

ArticleinEuropean Journal of Pediatric Surgery 17(4):285-8 · September 2007with3 Reads
Impact Factor: 0.99 · DOI: 10.1055/s-2006-924376 · Source: PubMed

    Abstract

    Desmoid tumours, also known as aggressive fibromatosis, are rare lesions with an intermediate biological behaviour between benign fibrous lesions and fibrosarcomas. Although abdominal desmoids have an increased incidence in Gardner's syndrome, they are rarely found in an isolated form. We report the findings of a barium study, ultrasound, computed tomography and magnetic resonance imaging in a nine-year-old boy with intermittent nausea and vomiting, diagnosed as having a desmoid tumour. Although intra-abdominal desmoids are usually detected as a solitary lesion in sporadic cases, the presented case had two mesenteric lesions in the left upper quadrant. There was intestinal obstruction and the masses had invaded the colon wall.