Atypical presentation of atypical amyloid

Department of Pathology University of Pittsburgh Medical Center-Montefiore, Pittsburgh, PA, USA.
Nephrology Dialysis Transplantation (Impact Factor: 3.58). 10/2010; 26(1):373-6. DOI: 10.1093/ndt/gfq638
Source: PubMed


Amyloidosis is a group of diseases categorized by precipitation of a group of protein aggregates (amyloid) in tissues, including
the kidney, and proteinuria is usually the commonest, though not exclusive, hallmark of clinical presentation. AL and AA are
the most commonly recognized forms of amyloidosis involving the kidney, but other forms have been described. We present a
case of renal amyloidosis due to a novel amyloidogenic protein, leucocyte cell-derived chemotaxin 2, without proteinuria at
presentation or on subsequent follow-up.

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Available from: Danniele Holanda
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