Sickle Cell Disease: An Opportunity for Palliative Care Across the Life Span

Department of Biobehavioral Health Science (MC 802), Center for End-of-Life Transition Research, University of Illinois at Chicago, 845 South Damen Avenue, Room 660, Chicago, IL 60612-7350, USA.
Nursing Clinics of North America (Impact Factor: 0.84). 09/2010; 45(3):375-97. DOI: 10.1016/j.cnur.2010.03.003
Source: PubMed


Sickle cell disease is a chronic illness that affects patients physically and emotionally and can do so at an early age. An ecological model of palliative care that involves improved communication among the health care team, patients, and their families can be beneficial. Open and honest communication regarding advance care planning, disease management, relief of pain and other symptoms, and bereavement and grief are all important for the patient, family, and health care team. Given the multiple acute and chronic complications of sickle cell disease, an approach to care that is holistic and comprehensive may help to improve a patient's biologic function and the perceived health, functional status, and quality of life of the patient and family.

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Available from: Robert Molokie, May 06, 2014
    • "She mentioned that PC should be, at least, integrated into the care of patients with severe SCD to deliver better end-of-life care.[8] Benjamin and Wilkie et al. suggested a multidisciplinary PC approach throughout the disease trajectory which may start at diagnosis of SCD.[1618] "
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    ABSTRACT: The palliative care (PC) needs of patients with noncancer life-threatening illnesses are comparable to that of cancer patients. This report describes the contribution of noncancer patients to the population of PC patients in a tertiary care hospital in the Eastern Province of Saudi Arabia. This is a retrospective review of the "palliative care inpatient database" of 21 months. From 474 patients, 20 (4.2%) had a noncancer diagnosis. The main reason for the referral of noncancer patients was pain control. The most prevalent diagnoses were sickle cell disease (SCD) in 6 (30%) patients and peripheral arterial disease (PAD) in 5 (25%). These findings suggest that the PC needs of noncancer patients are largely unmet in our region. Further efforts are necessary to advance noncancer PC in Saudi Arabia. The PC needs of patients with SCD and PAD need to be addressed in future research.
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