Plummer-Vinson syndrome in children. A report of three cases.

ArticleinLa Semaine des hôpitaux de Paris 75(3-4):74-77 · February 1999
Abstract
Three cases of Plummer-Vinson syndrome in girls aged 11 to 15 years are reported. All three patients presented with proximal dysphagia and chronic anemia. The exact role of iron deficiency in Plummer-Vinson syndrome remains unclear. The diagnosis rests on demonstration of an esophageal web by opacification or endoscopic evaluation of the esophagus, The dysphagia and the esophageal constriction resolve after iron store replenishment, Plummer-Vinson syndrome is associated with a high risk of esophageal cancer.
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