Chronic catastrophic-like antiphospholipid syndrome: A " smoldering" variant?

ArticleinRheumatology International 30(1):123-5 · May 2009with3 Reads
Impact Factor: 1.52 · DOI: 10.1007/s00296-009-0913-8 · Source: PubMed

    Abstract

    Catastrophic antiphospholipid syndrome (CAPS) is characterized by life-threatening diffuse thrombotic manifestations involving particularly small vessels of kidney, lungs, brain and skin. We report a 20-year-old female with systemic lupus erythematosus and secondary antiphospholipid syndrome who presented typical organ and histological involvement as seen in CAPS but with protracted course suggesting a “smoldering” form of the disease.