Unique Case of Giant Adult Paratesticular Spindle Cell Rhabdomyosarcoma

Università degli Studi di Bari Aldo Moro, Bari, Apulia, Italy
Urology (Impact Factor: 2.19). 12/2008; 73(3):500-2. DOI: 10.1016/j.urology.2008.09.025
Source: PubMed


A 50-year-old unmarried rural man was referred for a giant painless scrotal lump which had developed over a period of about six years. At the admission physical examination disclosed a large swelling scrotum and palpable left supraclavicular lymph nodes. Blood counts, renal and hepatic function tests, lactate dehydrogenase, beta-HCG, and alpha-fetoprotein were normal. Computed tomographic scan of thorax and abdomen revealed supraclavicular, mediastinal, and retroperitoneal adenopathies. The patient underwent right-sided radical orchiectomy. The final pathological diagnosis was paratesticular spindle cell rhabdomyosarcoma. Unfortunately, few days after surgery, patient presented a clinical and laboratory picture of disseminated intravascular coagulation followed by exitus.

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