Unilateral progressive proptosis in neonate.

Department of Otolaryngology, Post Graduate Institute for Medical Education and Research, Chandigarh, India.
Indian Journal of Otolaryngology and Head & Neck Surgery (Impact Factor: 0.05). 01/2004; 56(1):35-6. DOI: 10.1007/BF02968770
Source: PubMed


Orbital teratomas are congenital germ cell tumors that present at birth or within the first few months of life with unilateral proptosis. Primary orbital teratomas produce diffuse enlargement of the orbit. Orbital teratoma contains a wide diversity of tissues ranging from undifferentiated mass of tissue to a fully differentiated fetus in fetus. The tumor components are derived from two or more germinal layers. Most teratomas are cytnlogically benign, having both cystic and solid areas and on occasions may undergo a malignant change. Most patients in the past have been treated by orbital exenteration. We report a case of orbital teratoma that rapidly progressed over a course of days.

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