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ABSTRACT: Rickets is an unusual disorder in international adoptees. Three international adoptees from the former Soviet Union recently presented with rickets. Their clinical and laboratory presentations were atypical, reflecting circumstances unique to children adopted from orphanages in the former Soviet Union and the early initiation of vitamin D therapy. In these children, radiographs of the long bones were diagnostic when the classically diagnostic biochemical parameters, calcium and 25OHD(3) levels, were normal.
PEDIATRICS 01/2001; 106(6):1484-8. · 4.47 Impact Factor
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ABSTRACT: We reevaluated seven patients who initially had been managed nonoperatively because of a progressive valgus deformity that had occurred within approximately twelve months after satisfactory healing of a proximal tibial metaphyseal fracture sustained at an average age of four years (range, eleven months to six years and four months). All seven patients were described in a previous report from our institution, published in 1986. In that report, spontaneous improvement of the angulation was documented after an average duration of follow-up of thirty-nine months and nonoperative treatment of the deformity was recommended.
The patients were followed radiographically for an average of fifteen years and three months (range, ten years and four months to nineteen years and eleven months) after the injury. The radiographs were reviewed to determine the metaphyseal-diaphyseal angle, the mechanical tibiofemoral angle, the proximal and distal tibial remodeling angles, the limb-length discrepancy, and the deviation of the mechanical axis of the limb from the center of the knee joint. Knee function was assessed with use of the rating system of the Cincinnati Sportsmedicine and Orthopaedic Center, and ankle function was assessed with use of the rating system of the American Orthopaedic Foot and Ankle Society.
Every patient had spontaneous improvement of the metaphyseal-diaphyseal and mechanical tibiofemoral angles. Most of the correction occurred at the proximal part of the tibia. The mechanical axis of the limb remained lateral to the center of the knee joint in every patient, with an average deviation of fifteen millimeters (range, three to twenty-four millimeters). The affected tibia was longer than the contralateral tibia in every patient, with an average limb-length discrepancy of nine millimeters (range, three to eighteen millimeters). The knee score on the affected side was excellent for five patients and fair for two; one of the patients who had a fair score had had a tibial osteotomy at the age of sixteen years because of pain in the lateral aspect of the knee that was thought to be due to malalignment. The ankle score on the affected side was excellent for three patients and good for four.
Spontaneous improvement of the deformity occurred in all patients and resulted in a clinically well aligned, asymptomatic limb in most. We believe that patients who have posttraumatic tibia valga should be followed through skeletal maturity and that operative intervention should be reserved for patients who have symptoms secondary to malalignment.
The Journal of Bone and Joint Surgery 07/1999; 81(6):799-810. · 3.27 Impact Factor
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ABSTRACT: The Pemberton osteotomy involves cutting directly into the iliopubic and ilioischial limbs of the triradiate cartilage of the acetabulum. Complete closure of the triradiate cartilage after this osteotomy has been described in case reports. The present experimental study was performed to determine whether physeal osseous bars formed after Pemberton osteotomy. Eight Pemberton osteotomies were performed in six piglets. The animals were killed, and the acetabula were studied with use of radiography, computed tomography, and histological analysis for evidence of physeal injury. Plain anteroposterior radiographs of the pelvis did not clearly demonstrate the formation of osseous bars. However, Bucholz radiographs, made with the acetabulum placed directly on the cassette, showed osseous bars in three of the four specimens that were studied in this manner. Histological sections of the eight specimens of triradiate cartilage demonstrated five osseous bars in the iliopubic limb and four in the ilioischial limb. In two specimens, there was disruption of the cartilage without osseous bridging. Only two of the eight specimens had normal histological findings in both the iliopubic and the ilioischial limb of the triradiate cartilage.
The Journal of Bone and Joint Surgery 03/1999; 81(2):169-76. · 3.27 Impact Factor
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ABSTRACT: We describe a mother and son with multiple, non-progressive, congenital contractures, camptodactyly and absent flexion creases, expressionless face, blepharophimosis, microstomia, and short stature. Although these cases share similarities with the autosomal-recessive Schwartz-Jampel and Marden-Walker syndromes, they have a different mode of inheritance and lack myotonia, one of the most characteristic findings of the Schwartz-Jampel syndrome. Our cases most closely resemble those previously reported as distal arthrogryposis type IIb, although in our patients the proximal joints are severely affected and extraocular involvement is absent. Hearing loss is present in one and cleft palate in the other of our patients; these findings were previously described in arthrogryposis syndromes other than type IIb. We suggest extending the spectrum of distal arthrogryposis to include these manifestations, since there appears to be significantly overlap between the different syndromes.
American Journal of Medical Genetics 12/1996; 65(4):286-90.
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The Journal of Bone and Joint Surgery 04/1995; 77(3):488-9. · 3.27 Impact Factor
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ABSTRACT: A system was designed to measure forces during femoral lengthening using force transducers on an Ilizarov femoral frame. Measurements were made in three teenaged subjects overnight and during weight bearing. A progressive increase in axial load secondary to distraction was seen, forces peaking at 428, 447, and 673 N for the three subjects. Little change in force transmitted by the frame was observed during weight bearing. Measurements taken before and after each individual lengthening showed no change in axial force or bending moment (p > 0.01). A diurnal variation of axial load was found (p < 0.01). Forces at midnight were greater than in the morning in all the subjects, with a mean difference of 113 N (p < 0.01). Distraction forces measured in the femur during distraction are greater than those previously measured in the tibia. Evidence exists that the callus is stiff and may be the origin of these forces.
Clinical Orthopaedics and Related Research 04/1994; · 2.53 Impact Factor
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Pediatric Radiology 02/1993; 23(5):391-4. · 1.67 Impact Factor
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ABSTRACT: This report describes an intraosseous maple branch fragment which presented on initial radiographs as a benign appearing lytic bone lesion. Sonography and CT confirmed the presence of intraosseous and intra-articular foreign body and chronic foreign body reaction.
Pediatric Radiology 02/1991; 21(6):457-8. · 1.67 Impact Factor
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ABSTRACT: Bilateral radiographic irregularities and deformities of the proximal femoral epiphyses are features of both multiple epiphyseal dysplasia and bilateral idiopathic avascular necrosis. In the past these entities have been difficult to differentiate. This report documents radiographically the occurrence of avascular necrosis in 10 patients with multiple epiphyseal dysplasia by recognizing the super-imposition of sclerosis and subchondral fissuring on pre-existing symmetrically irregular proximal femoral ossification centers. Scintigraphic (photopenia) or magnetic resonance (loss of signal) criteria of avascular necrosis confirm its added presence and help to establish an imaging scheme to identify avascular necrosis superimposed on multiple epiphyseal dysplasia.
Skeletal Radiology 02/1989; 18(4):273-81. · 1.54 Impact Factor
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ABSTRACT: This is a review of 48 patients registered in the University of British Columbia Bone Tumour Registry as having eosinophilic granuloma, with emphasis on the historical development, treatment and results. Comments on the place of scintigraphic imaging are included. Eosinophilic granuloma in its solitary form is a self-limiting disease requiring no treatment. It can, however, progress to multifocal disease or the historically important triad known as Hand-Schüller-Christian syndrome. There is some evidence that it may have an immunologic basis, but the authors have little new to offer with respect to its etiology.
Canadian journal of surgery. Journal canadien de chirurgie 08/1988; 31(4):264-7. · 1.05 Impact Factor
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ABSTRACT: The developing hip in children with osteochondrodysplasias has not been well-described because of delayed ossification and limitations of conventional radiologic techniques. Twenty-four children with various osteochondrodysplasias were evaluated by ultrasonography. Variation in the configuration of the acetabulum included a horizontal acetabular roof owing to delayed iliac development and a notched acetabular roof with lateral bone deficiency. All children had thickened acetabular cartilage except for one child with osteogenesis imperfecta. Coxa vara was a common finding. All neonates displayed a very small beta angle (mean, 42 degrees) because the labrum lay more vertically, secondary to deep engagement of the femoral head in the acetabulum. Proximal femoral ossification was delayed in most children, which allows use of ultrasonography at a later age than is possible in the normal pediatric population. Hip ultrasonography in children with skeletal dysplasias can aid in early diagnosis and is useful in assessing hip morphology and development.
Journal of Pediatric Orthopaedics 20(5):588-93. · 1.16 Impact Factor
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ABSTRACT: We observed radiographic changes of avascular necrosis (AVN) of the capital femoral epiphysis in 9 hips of 11 patients with multiple epiphyseal dysplasia (MED). Plain roentgenography, bone scintigraphy, and magnetic resonance imaging (MRI) studies all revealed characteristic asymmetric changes in the presence of AVN superimposed on dysplastic femoral heads.
Journal of Pediatric Orthopaedics 9(6):666-71. · 1.16 Impact Factor
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ABSTRACT: Factors affecting outcome after pediatric forearm fracture include fracture angulation and fracture position. A new index, axis deviation, combines these factors. Two review studies were performed to determine if axis deviation correlated with outcome. In the first study, 35 subjects were reviewed 2.7 years after fracture without radiographs. In the second study, 152 fractures were reviewed a mean of 4 years after fracture, with 124 patients consenting to undergo radiographs. In both studies, the new index, axis deviation, correlated better with restricted forearm movement than either degree of angulation or fracture position. Midshaft and distal remodeling occurred and could be predicted in terms of axis deviation. We propose that an axis deviation of < 5 at the time of union be the reduction criteria of pediatric forearm-shaft fracture regardless of fracture position.
Journal of Pediatric Orthopaedics 14(2):200-6. · 1.16 Impact Factor
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ABSTRACT: The case of a 7-year-old boy with Legg-Calve-Perthes disease is presented. He had a prominent island of superficial epiphyseal ossification in his right femoral head, an unusual finding in Legg-Calve-Perthes disease. Hip arthroscopy was used successfully to identify and treat the lesion. After the procedure, the patient had a reduction in pain and an increase in range of hip motion. We believe that this case demonstrates the effective use of hip arthroscopy in the treatment of this unusual sequela of Legg-Calve-Perthes disease.
Arthroscopy The Journal of Arthroscopic and Related Surgery 15(1):88-92. · 3.02 Impact Factor
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ABSTRACT: Reconstructive acetabular osteotomies can affect the acetabular volume. Volume mismatch between the femoral head and the acetabulum should be an important consideration but is rarely evaluated before hip reconstruction. Accurate measurement of the volume of the acetabulum is difficult because of the unusual shape and spatial orientation of the acetabulum. In this study, we used three techniques (physical, two-dimensional computed tomography, and three-dimensional computed tomography reconstruction) to determine the volume of 18 pig, four sheep, and 15 model acetabulae. A comparison of pre- and post-Pemberton osteotomy volumes of three dysplastic acetabulae models and two patients with developmental dysplasia of the hip also was performed. The results indicate that accurate, reproducible volume determinations can be made by using all three techniques, and that certain data-selection modes can reduce the patient's exposure to radiation. In addition, we observed an increase in the volume of the acetabulum after the Pemberton osteotomy.
Journal of Pediatric Orthopaedics 18(5):657-61. · 1.16 Impact Factor
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ABSTRACT: We conducted an independent assessment of two clubfoot-classification systems. In a blinded trial, two orthopaedists scored 55 feet by using the classification systems developed by Pirani et al. and by Dimeglio et al. Thirty-seven of the feet were also scored by a physical therapist. By using the 10-point classification described by Pirani, the two physician examiners tallied total scores that were within one point of one another 89% of the time. The mean difference between the scores assigned by the two examiners was 0.6 points. For the 20-point classification described by Dimeglio et al., total scores tallied by the two physician examiners were within two points of one another 91% of the time. The mean difference between the scores assigned by the two physician examiners was 1.4 points. Correlation coefficients were 0.90 (p = 0.0001) for the Pirani classification, and 0.83 (p = 0.0001) for the Dimeglio classification. Correlation coefficients were much lower for the first 15 feet scored and were also lower when the therapist's scores were included. Overall, both classification systems had very good interobserver reliability after the initial learning phase.
Journal of Pediatric Orthopaedics 18(3):323-7. · 1.16 Impact Factor
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ABSTRACT: Thirteen (3.2%) of 410 patients seen in British Columbia's Children's Hospital in Vancouver from January 1984 to September 1992 with supracondylar fractures did so with an absence of a radial pulse in an otherwise well perfused hand. A combination of segmental pressure monitoring, color-flow duplex scanning, and magnetic resonance angiography (MRA) appears to be a valid, noninvasive, and safe technique in evaluating patency of the brachial artery and collateral circulation across the elbow. Based on this study, early revascularization of a pulseless otherwise well-perfused hand in children with type 3 supracondylar fractures, although technically feasible and safe, has a high rate of asymptomatic reocclusion and residual stenoses of the brachial artery. Therefore a period of close observation with frequent neurovascular checks should be completed before more invasive correction of this problem is contemplated.
Journal of Pediatric Orthopaedics 17(3):303-10. · 1.16 Impact Factor
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ABSTRACT: The outcome of a pediatric forearm fracture is related to the angulation of that fracture at the time of union. We discuss the factors affecting the position of the fracture at union. Three hundred forty-six children with 369 reductions of forearm fractures were reviewed retrospectively. Quality of reduction at the time of operation and loss of reduction during the period of cast immobilization were assessed using axis deviation. Loss of reduction had a greater influence on the final position of the fracture at union than did the position of the fracture at initial reduction. To ensure a satisfactory outcome, all pediatric forearm fractures should be monitored with radiologic review and remanipulation if their axis deviation is > 5 in younger patients or > 3 in patients with fractures close to or after growth-plate closure. Right forearm fractures in boys were identified as a subgroup at greater risk for redisplacement.
Journal of Pediatric Orthopaedics 17(3):332-6. · 1.16 Impact Factor
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ABSTRACT: Seven patients with total fibular hemimelia who underwent limb-lengthening procedures prior to skeletal maturity were evaluated for tibial and femoral growth after lengthening. The average preoperative follow-up was 6.5 years and all patients were followed to skeletal maturity. Thirteen segments (eight tibiae and five femora) were lengthened by three methods (Wagner, Ilizarov, and modified Ilizarov). The average preoperative limb-length discrepancy was 9.7 cm, and the average projected limb-length discrepancy at skeletal maturity was 12.5 cm. The average tibial lengthening was 6.7 cm (range, 5.3-10) with an average percentage of lengthening of 26% (range, 19-40%). The average postoperative growth rate of the tibia was 80% (range, 70-100%) and of the femur, 83% (range, 70-90%) of the normal side. Five tibiae showed a decrease in the average preoperative growth rate from 82.5% (range, 70-100%) to 39% (range, 26-54%) of the normal side. Two tibiae had no longitudinal growth after lengthening. The average postoperative growth rate of the femur decreased from 83% (range, 70-90%) to 61% (range, 26-125%). In one patient there was an increase in the rate of growth of the femur. These findings suggest that limb lengthening in skeletally immature children with total fibular hemimelia results in severe growth retardation of the tibia after lengthening. The subsequent growth of the tibia after lengthening in patients with total fibular hemimelia is unpredictable.
Journal of Pediatric Orthopaedics 16(4):438-44. · 1.16 Impact Factor
