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ABSTRACT: Gorlin syndrome is a rare autosomal dominant disorder characterized by multiple basal cell carcinomas of the skin, odontogenic keratocysts of the jaw, various skeletal abnormalities, and lamellar falx calsifications. Many associated lesions have been reported. In this report, we present a case of Gorlin syndrome with an osteoma in the maxillary sinus which has never been reported in the literature.
Tanısal ve girişimsel radyoloji: Tıbbi Görüntüleme ve Girişimsel Radyoloji Derneği yayın organı 01/2005; 10(4):268-71.
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ABSTRACT: To review the MR imaging findings of multicystic encephalomalacia and to investigate the correlation between MR imaging and clinical findings.
Twenty-one patients who presented with convulsion, mental-motor retardation and microcephaly and had evidence of multicystic encephalomalacia on MR images were included in this study. MR imaging patterns and clinical findings were reviewed. Consequently, we correlated MR imaging findings and clinical outcome.
All patients had cortical thinning, white matter destruction, atrophy and gliosis. Tetraplegia was seen in 17 out of 19 patients with mixed type cerebral palsy in two patients with diffuse or symmetric involvement on MR imaging. Both of the patients with mixed type cerebral palsy had basal ganglia involvement on MR imaging. Hemiplegia was seen in two patients with asymmetric involvement on MR imaging. Microcephaly was seen in 17 patients with diffuse or symmetrical, and in one patient with asymmetrical, involvement. Microcephaly and tetraplegia was seen in all patients with cerebellar and basal ganglion involvement.
Microcephaly and spastic tetraplegia were developed mostly in patients with diffuse involvement, whereas hemiplegia was seen in patients with asymmetric involvement. The clinical outcome was worse in patients with cerebellar and brainstem involvement. Therefore, we supposed that the symmetry of lesions and cerebellar or brainstem involvement might be used as a prognostic indicator.
Tanısal ve girişimsel radyoloji: Tıbbi Görüntüleme ve Girişimsel Radyoloji Derneği yayın organı 04/2004; 10(1):8-13.
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ABSTRACT: To evaluate the MR imaging findings of orbital hemangiomas in pediatric and adult groups.
MR imaging findings of seven orbital hemangiomas were reviewed. All patients had axial and coronal T1 and T2 weighted images. Axial and coronal fat suppressed (STIR) images and postcontrast T1 weighted images in three planes were obtained in order to evaluate the relation with surrounding structures. Localization, size, margins and signal characteristics of the lesions were analyzed.
Four of the cavernous hemangiomas were intraconal, one was extraconal. The location of the lesions was superomedial in two, middle medial, inferomedial and inferolateral in one lesion. The lesions were iso-hypointense to muscle on T1W, hyperintense on T2W and markedly hyperintense on STIR images. All cases had a capsule. In four cases a chemical shift artifact was seen. Contrast enhancement was patchy in early images and homogenous in late images. Cavernous hemangiomas were well circumscribed. All cases underwent operation and had a histopathologic diagnosis. The capillary hemangioma seen in a ten-year-old case was superomedial in localization and had irregular contours. The other case was a one year old. The lesion surrounded the superolateral margin of the bulbus and involved the lateral rectus, the eyelid and neighboring skin. The lesions were hypointense on T1W and hyperintense on T2W images, with diffuse homogenous contrast enhancement.
With MRI, orbital hemangiomas, the most common cause of chemosis and proptosis are easily detected. MR findings are not only helpful for diagnosing the lesion but also for choosing the appropriate surgical approach.
Tanısal ve girişimsel radyoloji: Tıbbi Görüntüleme ve Girişimsel Radyoloji Derneği yayın organı 04/2004; 10(1):26-30.
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ABSTRACT: Neurofibromatosis type 1 is characterized on magnetic resonance imaging by optic nerve gliomas, parenchymal gliomas, and foci of prolonged T2 relaxation involving the brainstem, cerebellum, midbrain, internal capsule, and basal ganglia. We report a child with neurofibromatosis type 1 in whom serial magnetic resonance imaging demonstrates spontaneous regression of basal ganglia lesions. These lesions, characterized on magnetic resonance imaging by increased signal intensity on T1- and T2-weighted sequences, involved the globus pallidus and internal capsules in a bilateral fashion.
Tanısal ve girişimsel radyoloji: Tıbbi Görüntüleme ve Girişimsel Radyoloji Derneği yayın organı 01/2004; 9(4):439-42.
