Article

Hemangiopericytoma of the spleen: Unusual presentation as multiple abscess

1Department of General Medicine, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
World Journal of Surgical Oncology (Impact Factor: 1.2). 02/2005; 3:77. DOI: 10.1186/1477-7819-3-77
Source: PubMed

ABSTRACT Hemangiopericytoma is a soft tissue vascular neoplasm arising from capillary pericytes and is found throughout the body in soft tissues and bone. It was first described in 1942. Primary vascular neoplasm of the spleen constitutes the majority of nonhaematolymphoid splenic tumors like haemangioma, lymphangioma, hemangioendothelioma, hemangiopericytoma etc. Splenic hemangiopericytoma is a rare tumor and probably first case was described in 1989. Uptill now only eight cases are reported in the English literature.
A-35-year old male presented with fever and dull aching pain in left hypochondriac region. Radiological evaluation showed presence of multiple abscesses in spleen. Investigations were done to rule out common causes of abscess in spleen. After failure of medical management, he was subjected to elective splenectomy. There were dense adhesions between the spleen and the adjacent structures and the diaphragm. The histopathology of the resected specimen showed hemangiopericytoma of spleen.
The present case illustrate that the hemangiopericytoma of spleen can mimic as multiple abscess. Splenectomy is the treatment of choice.

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Available from: Ajay K Khanna, Aug 04, 2015
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