Article

Thromboembolic renal infarction due to a renal artery aneurysm in a patient with Ehlers-Danlos syndrome type IV.

Department of Internal Medicine, Hadassah-Hebrew University Medical Center, Mount Scopus, Jerusalem, Z.C. 91240, Israel.
European Journal of Internal Medicine (impact factor: 2). 09/2006; 17(5):377-9. DOI:10.1016/j.ejim.2006.02.008 pp.377-9
Source: PubMed

ABSTRACT Type IV Ehlers-Danlos syndrome (EDS) is the only lethal form of EDS, mostly due to vascular complications. We describe a patient suffering from EDS type IV who presented with right thromboembolic renal infarctions due to a right renal artery aneurysm. We preferred observation to anticoagulation therapy because the thrombus in the renal artery aneurysm sealed the pending rupture of the arterial wall. This unusual embolic presentation of EDS exemplifies problematic aspects in the management of these patients.

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Keywords

arterial wall
 
EDS
 
EDS type IV
 
lethal form
 
patients
 
renal artery aneurysm
 
thromboembolic renal infarctions
 
Type IV Ehlers-Danlos syndrome
 
unusual embolic presentation
 
vascular complications