Primitive neuroectodermal tumor/extraosseous Ewing's sarcoma (PNET/EES) is a childhood disease rarely seen in adults. It is a soft tissue tumor, which is often observed in the paraspinal region and lower extremity. We report the case of a 32-year-old man who presented with sudden abdominal pain on the right upper quadrant that was radiated to the right flank. During the operation, a spontaneously ruptured right kidney mass was found. The histopathologic and immunohistochemical characteristics of the excised mass were consistent with PNET/EES. This is the first known reported case of spontaneously ruptured PNET/EES of the kidney with renal vein tumor thrombus. The clinical details and the management of this case are described.
"As far as literature reports, there are few reports of renal primitive neuroectodermal tumor/EWING with tumor thrombus extending to the inferior vena cava [9, 10]. However, in our case the thrombus extended all the way up to the inferior vena cava, right atrium, and bilateral pulmonary arteries, with more aggressive tumor extension than the previous reported cases [9, 10]. "
[Show abstract][Hide abstract] ABSTRACT: Only few cases of primary renal Ewing's sarcoma have been reported in the literature to date. We present here two cases of renal ES/PNET with an uncanny presentation. The first case was discovered after the patient presented clinically with irradiating flank pain, mimicking the pain related with kidney stones. The second case had clinical presentation of pulmonary thromboembolism after the patient was involved in an automobilist accident. The tumors were mainly composed of small blue cells which by immunohistochemical were positive for neural markers, and FISH revealed the translocation 22q12 for the EWSR1 gene. The diagnosis of renal primitive neuroectodermal tumor/EWING tumor is very rare and usually involves several different diagnostic techniques. The differential diagnosis is usually broad with frequent overlapping features between the entities. The cases presented in this paper illustrated the difficulties with which routine anatomical pathologist is faced when dealing with rare renal poorly differentiated neoplasm in adults.
Case Reports in Medicine 01/2012; 2012:190581. DOI:10.1155/2012/190581
[Show abstract][Hide abstract] ABSTRACT: The authors present an ISDN (integrated services digital network)
customer control capability, direct subscription parameter management
(DSPM). This capability would enable a user to directly set and later
modify values of certain subscription parameters that characterize the
services on that access line. This capability would consist of a
standard communications protocol on the D-channel and switch based data
verification and processing capabilities. Users could use of a range of
customer premise equipment (CPE) based applications in conjunction with
the network capabilities to perform real-time changes on many of the
ISDN subscription parameters. The capability for direct subscription
parameter management, in conjunction with the CPE based applications,
would provide the ISDN user with the ability to control and make
effective use of the extensive flexibility provided by ISDN, while
minimizing the need for BOC (Bell Operating Companies) service
Communications, 1990. ICC '90, Including Supercomm Technical Sessions. SUPERCOMM/ICC '90. Conference Record., IEEE International Conference on; 05/1990
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