Monophasic epithelial synovial sarcoma arising in the temporomandibular joint.

Division of Dentistry and Oral-Maxillofacial Surgery, Chiba University Hospital, 1-8-1 Inohana, Chiba 260-8677, Japan.
International Journal of Oral and Maxillofacial Surgery (Impact Factor: 1.36). 09/2007; 36(8):762-5. DOI: 10.1016/j.ijom.2007.02.014
Source: PubMed

ABSTRACT Synovial sarcoma is a mesenchymal spindle-cell tumour that occurs infrequently in the head and neck. It originates from unknown stem cells differentiating into mesenchymal and/or epithelial structures. Most synovial sarcomas are biphasic in character, consisting of epithelial and spindle-cell elements. Here is reported a case of monophasic epithelial synovial sarcoma arising in the temporomandibular joint. The tumour was of a predominantly epithelial pattern, although a minute area of sarcomatous cells was found. The primary mode of treatment was wide en-bloc excision. Two years after surgery, the patient died of hepatocellular carcinoma, but there was no evidence of synovial sarcoma recurrence.

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