Article

Idiopathic neuralgic amyotrophy in childhood.

Department of Neurology, University Hospital Maastricht, Maastricht, The Netherlands.
Neuropediatrics (Impact Factor: 1.19). 03/2007; 38(1):36-7. DOI: 10.1055/s-2007-981468
Source: PubMed

ABSTRACT In addition to the review by van Alfen et al., which has been published in 2000, we would like to report a seven-week-old boy with bilateral idiopathic brachial plexus neuropathy that did not show any signs of osteomyelitis on repeated scintigraphy. To our knowledge this is the first child reported with bilateral plexus involvement.

0 Bookmarks
 · 
55 Views
  • [Show abstract] [Hide abstract]
    ABSTRACT: A discussion is presented of the performance of the Smith delay compensator (SDC) of Smith predictor during the closed-loop operation of continuous linear systems with an appreciable time delay. The basic principle of the SDC is to design the closed-loop system in such a way that the system response is a delayed version of the delay-free system response, where the delay is the plant transport lag. Difficulties inherent in the SDC are briefly mentioned with suggestions to compensate for them. An example of the SDC scheme is illustrated in the closed-loop sodium nitroprusside regulation of postoperative blood pressure.
    01/1988;
  • [Show abstract] [Hide abstract]
    ABSTRACT: Idiopathic neuralgic amyotrophy (INA) is a neurological disorder with a suspected autoimmune cause, and is characterized by a sudden onset of pain and subsequent atrophies of the arm and shoulder muscles. It has rarely been documented in children, but it has been suggested that the prognostic outcome is worse in children compared with adults. We present a case and 4 year follow up of severe INA in a 12-year-old boy along with a thorough review of reported cases in children, to provide an overview of the paediatric phenotype and prognosis. The patient presented with severe pain and a subsequent paresis around the right shoulder girdle. Blood tests, MRI and X-ray of the shoulder were all normal. Electromyography revealed patchy denervation of individual nerves of the brachial plexus. At 5 months he started recovering, but full recovery was only achieved after 3-4 years. We then reviewed the literature and identified 58 paediatric cases of INA. In total, 63% made a full recovery, 25% made a partial, and 13% made no recovery. Overall, recovery was quick with a mean recovery time of 11.1 months. Specific preceding events such as osteomyelitis, viral- and upper airway infections were frequently associated with INA, but with an age dependent pattern. INA is a rare neurological disorder, especially in children. When compared with adults, pain and bilateral affection seems less common, and recovery is quick. Although limited by its retrospective nature, this review suggests that the paediatric phenotype is different and milder from that of adults. It also indicates a better prognosis in children than previously anticipated.
    European journal of paediatric neurology: EJPN: official journal of the European Paediatric Neurology Society 03/2010; 14(6):467-73. · 2.01 Impact Factor
  • [Show abstract] [Hide abstract]
    ABSTRACT: We report a 15-day-old neonate with a brachial plexus neuropathy diagnosed as neuralgic amyotrophy concomitant with an osteomyelitis of the ipsilateral humerus. She was treated with intravenous antibiotics and oral dexamethasone and improved dramatically within days.
    European journal of paediatric neurology: EJPN: official journal of the European Paediatric Neurology Society 07/2008; 13(3):283-5. · 2.01 Impact Factor