Article

Red ear syndrome

Division of Neurology, Department of Medicine, Dalhousie University, QEII Health Sciences Center, Halifax, Nova Scotia, B3H 3Y9, Canada.
Current Pain and Headache Reports (Impact Factor: 2.26). 09/2007; 11(4):313-6. DOI: 10.1007/s11916-007-0210-8
Source: PubMed

ABSTRACT The red ear syndrome is a rare syndrome originally described by Lance in 1994. It involves pain in and around the ear and associated autonomic phenomena, the most significant of which is cutaneous erythema of the ear ipsilateral to the pain and obvious to the patient and examiner during the attack. It may well represent an auriculo-autonomic cephalgia and/or be part of the group of disorders recognized as trigeminal autonomic cephalalgias. As a syndrome, it still lacks specificity in regard to etiology, mechanisms, and treatment but is important to recognize clinically because of its associations.

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