Embryonal rhabdomyosarcoma of the biliary tree mimicking a choledochal cyst

Department of Radiation Oncology, Tata Memorial Hospital, Mumbai, India.
Journal of cancer research and therapeutics (Impact Factor: 0.79). 01/2007; 3(1):40-2. DOI: 10.4103/0973-1482.31971
Source: PubMed


Embryonal rhabdomyosarcoma (ERMS) of biliary tree is a rare type of mesenchymal neoplasm diagnosed at surgery or by preoperative liver biopsy. We present a one year eight months old child who mimicked a choledochal cyst and was eventually treated with surgery, chemotherapy with IRS IV protocol and adjuvant postoperative radiotherapy to surgical bed with 6 MV photons to a dose of 5040 cGy in 28 fractions.

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