Relief of severe retro-orbital pain and vision improvement after optic-nerve decompression in polyostotic fibrous dysplasia: Case report and review of the literature

Department of Neurosurgery, Royal Liverpool Children's Hospital, Alder Hey, Eaton Road, Liverpool, L12 2AP, UK.
Child s Nervous System (Impact Factor: 1.11). 05/2008; 24(4):515-20. DOI: 10.1007/s00381-007-0543-y
Source: PubMed


We describe a case of a 9-year-old girl who developed progressive severe retro-orbital pain and partial visual loss in association with left optic-nerve compression due to polyostotic fibrous dysplasia of the skull.
Intradural decompression of the optic nerve resulted in immediate and complete resolution of the pain as well as a vast visual improvement.
In cases of fibrous dysplasia of the skull with evidence of optic-nerve compression, relief of retro-orbital pain should be an additional consideration when deciding to proceed with surgical management.

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