Poland's syndrome

Division of Pediatric Surgery, Mayo Clinic, 200 First Street SW, Rochester, MN 55905, USA. <>
Seminars in Pediatric Surgery (Impact Factor: 1.94). 09/2008; 17(3):161-6. DOI: 10.1053/j.sempedsurg.2008.03.005
Source: PubMed

ABSTRACT The main purpose of surgical correction in Poland's syndrome is to improve chest wall symmetry and correct breast hypoplasia. Creation of an anterior axillary fold and smoothing out the infraclavicular defect greatly improves the final result. Cardiorespiratory function may be impaired, but serious conditions requiring early operative correction are rare. When present, unilateral costochondral agenesis involves one to three segments in the mid-anterior chest and sternal depression to that side. Operative planning in such cases includes a multi-layered approach to provide a solid base for soft tissue reconstruction of the more superficial layers.

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    ABSTRACT: Classical Poland Syndrome (PS) is characterized by unilateral, partial or complete absence of the sternocostal head of the major pectoral muscle and brachysyndactyly of fingers on the same side. We report the case of a newborn infant with dextrocardia and PS located on the left side. This association is very rare: to date only 19 cases have been described in scientific literature. In all reported cases, as in the present, the Poland defect involved the left side and was associated to rib defects, whereas most cases of PS are on the right side and few have rib defects. This case supports the view that dextrocardia follows the loss of volume of the left hemithorax caused by Poland sequence and that the combination of PS and dextrocardia is not coincidental.
    Italian Journal of Pediatrics 02/2010; 36:21. DOI:10.1186/1824-7288-36-21
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    ABSTRACT: Purpose: Poland syndrome is rare disease which is characterized by absence of unilateral pertoralis major muscle accompanied by ipsilateral syndactyly or brachydactyly, which was described first by Alfred Poland in 1841. Materials and Methods: We performed the physical examination, laboratory test and radiologic evaluation to 18 year old male, who complaint asymmetry of right anterior chest. Results: We diagnosed the Poland syndrome due to absence of right pectoralis major muscle and brachydactyly of right hand. Conclusion: Current authors report a patient who had hypopalsia of pectoralis muscles, which needed differential diagnosis with pectoralis major rupture.
    06/2010; 13(1). DOI:10.5397/CiSE.2010.13.1.123
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    ABSTRACT: Poland's syndrome comprises a spectrum of chest-wall deformities affecting, to various degrees, the rib cage, the chest-wall muscles, neurovascular structures of the ipsilateral arm and the overlying breast. We present a neonate with features of depressed right chest-wall with no respiratory distress. Computed tomography showed hypolasia of the right pectoralis major muscle, with reduced subcutaneous fat on the ipsilateral side of the chest, with abnormalities of the ribs on the same side but absent upper limb deformities. There is negative history of other family members of being affected.
    04/2014; 3(1):44-6. DOI:10.4103/2249-4847.128735