Partial internal biliary diversion for patients with progressive familial intrahepatic cholestasis type 1.

Division of Pediatric Surgery, Department of Surgery, Nagasaki University Graduate School of Biomedical Sciences, 1-7-1 Sakamoto, Nagasaki, 852-8501, Japan.
Pediatric Surgery International (Impact Factor: 1.22). 01/2012; 28(1):51-4. DOI: 10.1007/s00383-011-3018-x
Source: PubMed

ABSTRACT We herein report a case of progressive familial intrahepatic cholestasis with partial internal biliary diversion (PIBD). Although by using PIBD an external stoma can be avoided, exposure of the ileocecal junction to bile reflux as well as the effects of the direct bile flow on the colonic mucosa require further investigation.

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