POEMS syndrome associated with multiple hemangiomas of the small bowel and colon.

Department of Medicine B, Westfälische Wilhelms-Universität, Münster, Germany.
Endoscopy (Impact Factor: 5.05). 09/2008; 40 Suppl 2:E134. DOI: 10.1055/s-2007-995686
Source: PubMed
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    ABSTRACT: POEMS syndrome is a rare multi-system disease with typical features of polyneuropathy, organomegaly, endocrinopathy, monoclonal plasmaproliferative disorder and skin changes. We describe a 44-year-old woman with polyneuropathy, hepatomegaly, IgA lambda-plasmacytoma, thrombocytosis, papilledema with elevated protein levels in cerebrospinal fluid and multiple cutaneous hemangiomas who was diagnosed with three intracranial lesions. Histology revealed capillary hemangiomas, one of them displaying partially glomeruloid features.
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