Rosai-Dorfman disease: Sinus histiocytosis with massive lymphadenopathy

ENT, Kartal Dr. Lutfi Kirdar Training and Research Hospital, Istanbul, 34870, Turkey.
Case Reports 05/2009; 2009. DOI: 10.1136/bcr.11.2008.1251
Source: PubMed

ABSTRACT A 25-year-old man presented with a 3 month history of a painless mass on the right side of his neck. Physical examination revealed a smooth surfaced, bilobed, 4×3 cm, semimobile mass at the right and 3×2 cm at the left jugulodigastric region. Endoscopic examination of the patient showed a granular tumour in both nasal cavities. After biopsies were taken from the mass from the nasal cavity, a diagnosis of Rosai-Dorfman disease was made. A conservative approach was taken to treatment and after the 6 month follow-up period, the patient was in a stable condition.

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