Intraosseous CSF Fistula in a Patient with Gorham Disease Resulting in Intracranial Hypotension

Department of Radiology and Biomedical Imaging, University of California, San Francisco, CA, USA.
American Journal of Neuroradiology (Impact Factor: 3.59). 06/2011; 32(11):E198-200. DOI: 10.3174/ajnr.A2413
Source: PubMed


A 7-year-old girl with a history of headaches and Gorham disease was surgically treated in infancy for Chiari I malformation. Subsequent investigation revealed that her cerebellar tonsillar ectopia was due to a long-standing spinal CSF-lymphatic fistula causing intracranial hypotension. Percutaneous fistula closure was performed several times, resulting in transient symptomatic improvement.

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