Intracranial rosai-dorfman: A clinical challenge

Department of Hematology Oncology, Staten Island University Hospital, Staten Island, NY 10305, USA.
The Neurologist (Impact Factor: 1.16). 03/2011; 17(2):117-9. DOI: 10.1097/NRL.0b013e31820a9e02
Source: PubMed


Rosai-Dorfman disease has been described as massive painless cervical lymphadenopathy with a benign clinical course and unclear etiology. Isolated extranodal involvement has been rarely described. We present a rare case of isolated intracranial Rosai-Dorfman disease that was diagnosed and treated at our institution. Our diagnostic and clinical challenges are presented with a review of the literature.

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