[Show abstract][Hide abstract] ABSTRACT: Severe hemophilic patients are prone to develop long-term sequelae such as pseudotumor formation caused by repeated and unresolved hematomas leading to subsequent encapsulated mass lesion. Among these, renal hemophilic pseudotumors are seen as a rather rare event. Once developed, this serious condition should be approached carefully, first by maintaining adequate hemostasis with appropriate factor replacement therapy and, later on, complete surgical excision should be targeted. Without surgical intervention, complete resolution is generally not possible. Other treatment modalities such as radiotherapy may be helpful in addition to surgery preoperatively in order to reduce bleeding complications. However, experience of this approach is limited to those pseudotumors of other sites such as bone and pelvic pseudotumors. Rarely, a true pseudotumor may mimic a malignancy; therefore, accurate assessment by radiological means is required. Considering the difficulties in management, it is of great importance to constitute early substitutive treatment for the prevention of pseudotumors.
Journal of Coagulation Disorders. 01/2009;
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