Calcifying fibrous pseudotumours: an unusual case with multiple pleural and mediastinal lesions

Department of Histopathology, Royal Devon and Exeter Foundation Hospital, Exeter, UK.
Interactive Cardiovascular and Thoracic Surgery (Impact Factor: 1.16). 12/2009; 10(4):652-3. DOI: 10.1510/icvts.2009.211581
Source: PubMed


Calcifying fibrous pseudotumour (CFPT) is a rare soft tissue lesion that has been reported in the pleura and mediastinum. The literature contains reports of multiple pleural lesions. We describe a case of a 22-year-old woman with multiple bilateral pleural and mediastinal CFPTs. The diagnosis was established following the resection of multiple lesions. However, many lesions remain. We discuss the clinical behaviour of CFPTs and the dilemma of leaving remaining lesions in situ. (c) 2010 Published by European Association for Cardio-Thoracic Surgery. All rights reserved.

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