Displasia fibrosa de seio maxilar

Arquivos Internacionais de Otorrinolaringologia 01/2009;
Source: DOAJ


Introdução: A Displasia Fibrosa é uma doença benigna do osso, de crescimento lento e etiologia desconhecida. O envolvimento do esqueleto craniofacial não é incomum e, geralmente, produz assimetrias faciais. Relato do Caso: Neste artigo relatamos o caso de um paciente com displasia fibrosa ocupando todo o seio maxilar esquerdo com extensão orbitária confirmado pelo anatomopatológico. Comentários Finais: O tratamento cirúrgico permanece como principal abordagem terapêutica e o seguimento pós-cirúrgico faz-se necessário pelo caráter recidivante desta condição.

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    ABSTRACT: we present the case of a localized monostotic fibrous dysplasia in the frontal sinus with orbital extension and persistency after the first surgery; it had to be operated again with a fronto-orbitary reconstruction. the fibrous dysplasia is a rare bony alteration with transformation of the healthy bony tissue for a disestructuredone. its etiology is unknown and can be associated to different syndromes, such as albright´s disease. its treatment is surgical, but presents a high percentage of recurrence, this is the xenson why it needs a close follow up
    Acta Otorrinolaringológica Española 12/2002; 53(3):203–206. DOI:10.1016/S0001-6519(02)78301-5


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