An unusual case of non-syndromic occurrence of multiple dental anomalies.

Department of Pedodontics and Preventive Dentistry, Manipal College of Dental Sciences, Mangalore, Manipal University, India.
Indian journal of dental research: official publication of Indian Society for Dental Research 01/2009; 20(3):385-7. DOI: 10.4103/0970-9290.57364
Source: PubMed

ABSTRACT Dental anomalies have been known to occur in humans due to a variety of genetic and environmental factors. Combinations of dental anomalies are known to be associated with specific syndromes. A few cases of multiple dental anomalies have been reported in patients with no generalized abnormalities. This case report describes an unusual occurrence of a combination of dental anomalies in an apparently normal healthy 12-year-old female patient. The dental anomalies in this patient were multiple dens invaginatus, generalized enamel hypoplasia, generalized microdontia, root resorption and multiple periapical lesions, shovel shaped incisors, cup shaped premolars, taurodontism, hypodontia and supernumerary teeth.

  • [Show abstract] [Hide abstract]
    ABSTRACT: Oral physician has always been challenged when it comes to diagnosing rare nonsyndromic cases because of the varied presentation of multiple dental abnormalities caused due to mutations in developmental regulatory genes. This coupled with skeletal abnormalities makes the task more difficult. But as we come across such rare constellation of findings, it makes the field more intriguing. Here, we report an extremely rare case of non syndromic occurrence of dental manifestations like multiple dens invaginatus, generalised microdontia, generalised hypoplasia, hypodontia, pulp stones and widening of pulp chamber along with skeletal findings of bilateral syndactyly of legs and brachydactyly of hands and legs. Although many non syndromic cases have been reported in the literature, the unusual occurrence of findings in the present case is being reported for the first time.
  • Source
    [Show abstract] [Hide abstract]
    ABSTRACT: Dental anomalies are the formative defects caused by genetic disturbances or environmental factors during tooth morphogenesis. Simultaneous occurrence of various multiple anomalies has been reported previously, particularly in cases of chromosomal abnormalities that often manifest with multisystem involvement. Very few cases of multiple anomalies have been documented in patients with no known generalized abnormalities. The present paper shows an unusual occurrence of a combination of dental anomalies like mandibular canine transmigration, taurodontism in permanent mandibular molars, congenital agenesis of 14 numbers of permanent teeth excluding third molars, canine impaction, primary molars with pyramidal roots, midline diastema and generalized microdontia in an apparently normal 13-year-old Indian girl.
    06/2012; 2012:426091. DOI:10.1155/2012/426091
  • [Show abstract] [Hide abstract]
    ABSTRACT: Developmental dental anomalies are marked deviations from the normal colour, contour, size, number, and the degree of the development of teeth. Local as well as systemic factors may be responsible for these developmental disturbances. Such influences may begin before or after birth and hence the deciduous or the permanent teeth may be affected. These anomalies not only affect the aesthetic appearance of the teeth but also pose difficulties during the dental treatment and sometimes are the cause of dental problems.A rare case of dental developmental fusion of the permanent right lateral incisor with two supernumerary teeth, with dens invagination, dilacerations, talon's cusp and a periradicular lesion reported to the Department of Oral Medicine and Radiology, NHDC.The clinical and the radiographical findings led to the diagnosis of fusion of the permanent lateral incisor with two supplementary teeth. All the 3 involved teeth showed dens invaginatus, dilacerations of the roots and a talons cusp with a chronic periapical lesion.The rarity with which this entity appears, along with its complex characteristics, often makes it difficult to treat. A multidisciplinary approach, with different specialists working together, can contribute to the success of a treatment plan.
    11/2012; 6(9):1603-5. DOI:10.7860/JCDR/2012/4174.2576