Manifestaciones orales del síndrome de Mobius asociado a Poland: descripción de un caso clínico

Avances en odontoestomatologia 01/2009; 25(4). DOI: 10.4321/S0213-12852009000400002
Source: OAI


El síndrome de Mobius es una anomalía congénita que causa parálisis de los nervios VI y VII pares craneanos. Se caracteriza por malformaciones límbicas y cráneo-buco-faciales. Asociada a Poland, presenta malformación del músculo pectoral mayor y anomalías en pies y manos. Por ser un síndrome que presenta anomalías faciales y orales importantes como paladar ojival, mordida abierta, xerostomía, úvula bífida, malformaciones en la lengua, se destaca la necesidad de un abordaje odontológico eficaz con el fin de establecer una adecuada salud oral y calidad de vida del paciente. En este trabajo, descripción de un caso clínico, se expone los aspectos clínicos generales y orales, así como el tratamiento odontológico realizado en una paciente portadora del síndrome Mobius/Poland. Un abordaje enfocado en la orientación del responsable y en el control de la caries y la enfermedad periodontal, encontró una reducción significativa en los índices de placa bacteriana y sangrado gingival. Actualmente la paciente se encuentra en fase de mantenimiento. Como no hay cura para el síndrome, el tratamiento es enfocado al control y mantenimiento de las manifestaciones orales.

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