Spontaneous rupture of solid pseudopapillary neoplasm of the pancreas during pregnancy

Obstetrics and Gynecology (Impact Factor: 5.18). 01/2013; 121(2 Pt 2 Suppl 1):486-8. DOI: 10.1097/AOG.0b013e31826d292f


Spontaneous rupture of solid pseudopapillary neoplasm of the pancreas is an unusual complication during pregnancy.

At 19 weeks of gestation, a 29-year-old woman presented with a pancreatic mass and upper abdominal pain radiating to the back. On the third day of admission, shock and peritoneal signs developed. Exploratory laparotomy and subsequent subtotal pancreatectomy were performed for a bleeding tumor. Solid pseudopapillary neoplasm was confirmed by pathological examination. The patient delivered a healthy full-term girl vaginally. Eight months postoperatively, the clinical courses of both mother and infant have been uneventful.

Ruptured solid pseudopapillary neoplasms can cause an acute abdomen during pregnancy. The expression of progesterone receptors in solid pseudopapillary neoplasm is a possible cause of this potentially devastating event.

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