True duplicate bladder exstrophy: a rare lesion.

Department of Pediatric Surgery, Sir Padampat Mother and Child Health Institute, (JayKayLon Hospital) S.M.S. Medical College, Jaipur 302004, Rajasthan, India.
The Indian Journal of Pediatrics (Impact Factor: 0.72). 08/2009; 76(8):852-3. DOI: 10.1007/s12098-009-0172-4
Source: PubMed

ABSTRACT A two-day-old newborn male child with a rare variant of exstrophy bladder was managed in our institute. The child has true duplicate bladder exstrophy which is extremely rare and only 8 cases reported in the world literature so far. We describe another one and briefly review the literature.

  • [Show abstract] [Hide abstract]
    ABSTRACT: To describe a unique approach to the management of duplicate bladder exstrophy combining initial bladder closure and epispadias repair. Bladder exstrophy has been successfully managed by staged surgical repair with early bladder closure, subsequent epispadias repair, and, finally, bladder neck reconstruction. Duplicate bladder exstrophy is a rare variant of the exstrophy complex with fewer than 20 cases reported. A male newborn presented with the appearance of both bladder exstrophy and a ruptured omphalocele. Repair of the omphalocele and bilateral orchiopexy was performed shortly after birth, but bladder closure was delayed until there was complete healing of the omphalocele defect, and the investigators believed the infant was ready for abdominal wall and bladder exstrophy closure. At age 8 months, bladder closure was performed with the intraoperative finding of a duplicate bladder lying posterior to the exstrophied bladder. The left ureter drained on the exstrophic bladder plate, and the right ureter drained into the posterior (internalized) duplicate bladder. After anterior innominate and vertical iliac osteotomies, the left ureter was reimplanted into the posterior bladder. A portion of the exstrophied bladder was then tubularized to construct a neourethra of the epispadic penis. The child has done well with an excellent cosmetic appearance of the abdominal wall and a straight phallus. The bladder subsequently required a Mitrofanoff-type continent stoma along with bladder augmentation, which was performed at the time of his Young-Dees-Leadbetter bladder neck reconstruction (age 3.5). The child is currently continent but requires intermittent clean catheterization through his appendicovesicostomy. The investigators report a unique and unexpected variant of bladder exstrophy and its successful management.
    Urology 03/1999; 53(2):401-4. · 2.42 Impact Factor
  • [Show abstract] [Hide abstract]
    ABSTRACT: Duplicate exstrophy of the bladder is a rare, distinct congenital anomaly without additional major anomalies of the urinary tract. A 15-year-old boy with duplicate exstrophy is reported on, and the possible role of bladder sequestration in the development of classical musculoskeletal deformities in this anomaly is discussed.
    Journal of Pediatric Surgery 05/1999; 34(4):626-7. · 1.38 Impact Factor
  • Plastic &amp Reconstructive Surgery 03/1963; 31(4):396. · 3.54 Impact Factor

Full-text (2 Sources)

Available from
Jun 4, 2014