Article

Meningoencefalocele transesfenoidal transpalatina

Arquivos de Neuro-Psiquiatria (Impact Factor: 1.01). 01/2006; DOI: 10.1590/S0004-282X2006000400020
Source: DOAJ

ABSTRACT A meningoencefalocele transesfenoidal é rara apresentação dos disrafismos do tubo neural. Caracteriza-se pela herniação do tecido neural através de uma falha óssea no osso esfenóide. A apresentação clínica é variável, podendo ser desde assintomática até obstrução das vias aéreas, rinorréia, meningite, disfunção hipotalâmica e anomalias ópticas. Seu tratamento cirúrgico é controverso. Descrevemos o caso de um menino de 7 anos que apresentava uma estrutura pulsátil preenchendo o teto da cavidade oral, disgenesia palatina e hipertelorismo. O diagnóstico de meningoencefalocele transesfenoidal transpalatina foi confirmado pela tomografia computadorizada e ressonância magnética. A criança foi operada com sucesso pela via transpalatal/transesfenoidal.

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