Primary Testicular Presentation of ALK-1–negative Anaplastic Large Cell Lymphoma in a Pediatric Patient

Department of Pediatrics, The Ohio State University College of Medicine, Columbus, OH, USA.
Journal of Pediatric Hematology/Oncology (Impact Factor: 0.9). 06/2009; 31(5):330-2. DOI: 10.1097/MPH.0b013e3181979c5e
Source: PubMed


Anaplastic large cell lymphoma is a heterogeneous group of malignant non-Hodgkin lymphomas that occurs in up to 15% of all pediatric non-Hodgkin lymphomas. It is characterized by B-symptoms and involvement of extranodal sites such as skin, bone, and soft tissue. This brief report describes first reported case of pediatric primary testicular anaplastic large cell lymphoma in a 14-year-old boy. The presentation included acute testicular pain, fever, and vomiting. After chemotherapy and unilateral radical orchiectomy, patient continues in complete remission.

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