Pseudoangiomatous Stromal Hyperplasia of the Vulva Presenting as a Polypoid Vulvar Lesion: A Lesion Associated With Anogenital Mammary-Like Tissue-Report of a Case and Review of the Literature.

Departments of 1Pathology and Laboratory Medicine, and 2Obstetrics, Gynecology, and Women's Health, University of Medicine and Dentistry of New Jersey, New Jersey Medical School, Newark, NJ.
Journal of Lower Genital Tract Disease (Impact Factor: 1.99). 04/2013; 17(4). DOI: 10.1097/LGT.0b013e31827a8aa2
Source: PubMed


The study aimed to report the case of a patient with a polypoid vulvar lesion clinically thought to be an aggressive angiomyxoma.

Materials and methods:
On examination, a 4.0 × 2.0 × 1.5-cm polypoid lesion was seen on the right labium majus.

Histopathological findings of the excised mass were consistent with pseudoangiomatous stromal hyperplasia of the vulva

Pseudoangiomatous stromal hyperplasia is a lesion of breast tissue but can occur in anogenital mammary-like glands. It must be distinguished from low-grade angiosarcoma.

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