Primary desmoplastic small round cell tumor of the kidney in a 7-year-old girl

Department of Urology, Children's Hospital Boston, 300 Longwood Avenue, HU-390, Boston, MA 02115, USA.
Journal of pediatric urology (Impact Factor: 0.9). 03/2006; 2(1):52-4. DOI: 10.1016/j.jpurol.2005.05.008
Source: PubMed


Desmoplastic small round cell tumor (DSRCT) is a rare pathologic entity that most frequently affects the peritoneal cavity and presents in adolescent boys. It often presents at an advanced stage and has a generally poor prognosis. We present an unusual case of DSRCT of the kidney presenting in a young girl. This is the first report of DSRCT of the kidney in the pediatric population, and it suggests that this condition should be a diagnostic consideration when assessing a child with a kidney mass.

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