Article

Retroperitoneal lipoblastoma: A discussion of current management

Texas Children's Hospital, Department of Pediatric Surgery, Baylor College of Medicine, Houston, TX.
Journal of Pediatric Surgery (Impact Factor: 1.31). 10/2012; 47(10):e51-4. DOI: 10.1016/j.jpedsurg.2012.07.052
Source: PubMed

ABSTRACT Retroperitoneal lipoblastomas are rare tumors found in young pediatric patients. Despite their large size at presentation, complete resection is usually achieved with minimal complications. Diagnosis is typically made after pathologic examination of the operative specimen, and cytogenetic analysis may be a key component in differentiating lipoblastoma from other lipomatous tumors. We present one such case of a large, retroperitoneal lipoblastoma and discuss the management of this uncommon entity.

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