Sturge-Weber syndrome with cerebellar involvement

Johns Hopkins Hospital, Baltimore, MD, USA.
Journal of Neuroradiology (Impact Factor: 1.75). 09/2008; 36(1):57-60. DOI: 10.1016/j.neurad.2008.07.008
Source: PubMed


Sturge-Weber syndrome is a rare neurocutaneous disorder that typically presents with angiomas involving the face, ocular choroid and ipsilateral supratentorial leptomeninges. Posterior fossa involvement is extremely rare. We present two patients with simultaneous supra- and infratentorial involvement. Magnetic resonance imaging (MRI) and digital subtracted angiography (DSA) findings are discussed.

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