Article

Sturge-Weber syndrome with cerebellar involvement.

Johns Hopkins Hospital, Baltimore, MD, USA.
Journal of Neuroradiology (impact factor: 1.21). 09/2008; 36(1):57-60. DOI:10.1016/j.neurad.2008.07.008 pp.57-60
Source: PubMed

ABSTRACT Sturge-Weber syndrome is a rare neurocutaneous disorder that typically presents with angiomas involving the face, ocular choroid and ipsilateral supratentorial leptomeninges. Posterior fossa involvement is extremely rare. We present two patients with simultaneous supra- and infratentorial involvement. Magnetic resonance imaging (MRI) and digital subtracted angiography (DSA) findings are discussed.

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Keywords

DSA
 
infratentorial involvement
 
Magnetic resonance imaging
 
MRI
 
ocular choroid
 
Posterior fossa involvement
 
rare neurocutaneous disorder
 
simultaneous supra-
 

M Smith Pearl