Article

Primäres diffuses Neurofibrom der Harnblase

Der Urologe (Impact Factor: 0.46). 01/2010; 49(11):1398-1400. DOI: 10.1007/s00120-010-2423-4

ABSTRACT Diffuse Neurofibrome sind gutartige mesenchymale Tumore mit Nervenscheidendifferenzierung. Es gibt lediglich sehr wenige Fallberichte
über diffuse Neurofibrome in der Harnblase. Wir präsentieren einen gut dokumentierten Fallbericht eines 62-jährigen Patienten,
der sich mit Makrohämaturie in unserer Klinik vorstellte. Die weitere Abklärung erbrachte den histologischen Nachweis eines
diffusen Neurofibroms. Wir führten daraufhin eine Literaturrecherche hinsichtlich klinischer Merkmale und therapeutischer
Optionen durch.

Diffuse neurofibromas are benign mesenchymal tumours with nerve sheath differentiation. Only a few cases have been reported
in the urinary bladder. We present a well-documented case report of a 62-year-old man presenting with gross haematuria and
histopathological confirmation of a diffuse neurofibroma. We further reviewed the current literature with regard to clinical
features and treatment options.

SchlüsselwörterDiffuses Neurofibrom-Harnblase-Fallbeschreibung
KeywordsNeurofibroma, diffuse-Bladder-Case report

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