[Plastic bronchitis in a ten year-old boy with Fontan circulation].
ABSTRACT Plastic bronchitis is a rare complication in children with inflammatory lung disease and postoperatively after Fontan operation for congenital heart disease. Plastic bronchitis is characterised by expectoration of large bronchial casts, which can cause fatal airway obstruction. We describe a case of a ten year-old boy with transposition vasorum and hypoplastic right ventricle who underwent a Fontan operation at the age of three. Seven years postoperatively he developed plastic bronchitis which was treated with mucolytics, inhaled corticosteroids, β2-agonist, hypertonic NaCl, and chest physiotherapy, resulting in partial recovery.