Congenital heterotopic gastrointestinal cyst of the oral cavity in a neonate: case report and review of literature.
ABSTRACT Heterotopic gastrointestinal cysts of the oral cavity are rare benign lesions which may mimic both benign and malignant neoplasms. These cysts are usually discovered during infancy, but may not appear until well into adulthood. This lesion involves the tongue and floor of the mouth in 97% of cases and has a male predilection. The cyst may range in size from less than 1 cm to 9 cm, with most lesions being 1-3 cm in size. About 30% of affected individuals have symptoms related to difficulties with feeding, swallowing and respiration. The epithelial lining is quite variable, but all cysts have an enteric lining. The histogenesis is related to entrapment of undifferentiated, noncommitted endoderm within the oral cavity during the 3rd-4th week of fetal life. The purpose of this paper is to report a congenital heterotopic gastrointestinal cyst of the oral cavity presenting in a neonate. The clinical and histopathologic features of this cyst are reviewed, as well as the histogenesis of this lesion.
- SourceAvailable from: Penelope F Brown
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- "Under the appropriate influences these pleuripotent cells can then differentiate into both gastrointestinal and respiratory structures in their new location. Other putative explanations have been described elsewhere  . In the majority of reported cases the patients have been under the age of 2, supporting the hypothesis that the cysts are congenital. "
ABSTRACT: The presence of normal alimentary tissue in an abnormal location is referred to as a heterotopic gastrointestinal cyst or duplication cyst. These are thought to be congenital and rarely occur in the neck. More often found in the oral cavity, they usually present as an asymptomatic swelling and are treated with surgical excision. We describe the rare presentation and diagnosis of an 8-month-old girl with a congenital heterotopic gastrointestinal cyst in the neck.International Journal of Pediatric Otorhinolaryngology Extra 09/2007; 2(3):154-157. DOI:10.1016/j.pedex.2007.04.005
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ABSTRACT: We describe the prenatal ultrasonographic features that led to the diagnosis of a lingual lymphangioma. The risk of upper airway obstruction, which is associated with this rare abnormality, prompted us to plan careful perinatal management. We believe that, in cases of suspected lymphangioma of the tongue or other oropharyngeal tumors, elective delivery should be carried out in a tertiary referral center in which emergency ventilation and tracheostomy are possible.Ultrasound in Obstetrics and Gynecology 02/1998; 11(2):141-3. DOI:10.1046/j.1469-0705.1998.11020141.x · 3.14 Impact Factor
- Journal of Pediatric and Adolescent Gynecology 05/1999; 12(2):114. DOI:10.1016/S1083-3188(99)80082-5 · 1.81 Impact Factor