Susac's syndrome: a rare cause of fluctuating sensorineural hearing loss.

Department of Otolaryngology-Head and Neck Surgery, University Hospital, Nottingham, UK.
The Journal of Laryngology & Otology (Impact Factor: 0.68). 12/1997; 111(11):1072-4. DOI: 10.1017/S0022215100139374
Source: PubMed

ABSTRACT Susac's syndrome is extremely rare and is characterized by the clinical triad of encephalopathy, retinal artery occlusion and deafness. A case of this rare syndrome is presented and for the first time the fluctuating nature of the hearing loss is demonstrated. The site and nature of the hearing loss has been investigated. The value of neural hearing loss as a method of monitoring the clinical severity is discussed.

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