Carcinomas of the thyroid and breast associated with Pendred's syndrome: report of a case.

Department of Surgery, Ankara Oncology Hospital, Demetevler, Turkey.
Surgery Today (Impact Factor: 1.53). 02/1998; 28(6):673-4. DOI: 10.1007/s005950050207
Source: PubMed


We report herein the case of a 49-year-old woman with Pendred's syndrome who developed follicular carcinoma of the thyroid and invasive ductal carcinoma of the breast. To the best of our knowledge, this is the first case of different primary neoplasms developing in a patient with Pendred's syndrome.

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    ABSTRACT: A case of Pendred's syndrome is reported. One year after subtotal removal of a simple adenomatous colloid goitre, the patient presented with a follicular thyroid carcinoma with invasive growth through the capsule into the surrounding muscular tissue and vascular invasion.
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