Extracutaneous Sweet syndrome involving the gastrointestinal tract in a patient with Fanconi anemia.

Division of Pathology and Laboratory Medicine, Our Lady's Hospital for Sick Children, Crumlin, Dublin, Ireland.
Journal of Pediatric Hematology/Oncology (Impact Factor: 0.96). 02/2001; 23(1):59-62. DOI: 10.1097/00043426-200101000-00015
Source: PubMed

ABSTRACT Acute febrile neutrophilic dermatosis, or Sweet syndrome, is a cutaneous eruption characterized clinically by the appearance of painful red plaques and nodules and histologically by an intense dermal neutrophilic infiltrate. Extracutaneous manifestations are rare. We report a patient in whom otherwise typical cutaneous Sweet syndrome was accompanied by an extracutaneous manifestation in the ileum.

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