Squamous cell carcinoma of the oesophagus in a patient with Klippel-Trenaunay syndrome.
ABSTRACT The Klippel-Trenaunay syndrome (KTS) is a rare disorder characterized by a triad of port-wine stains, varicose veins, and bony or soft tissue hypertrophy of one extremity. Digestive bleeding is the most commonly observed gastrointestinal manifestation. In rare cases, the syndrome is associated with malignancies. We report the case of a 38-year-old woman with KTS and dysphagia caused by an oesophageal squamous cell carcinoma.
- Pediatric Dermatology 04/1992; 9(1):80-2. · 1.04 Impact Factor
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ABSTRACT: The case of a patient affected by Klippel-Trenaunay syndrome presenting with esophageal variceal bleeding caused by hypoplasia of the vena porta is reported. Hemostasis was achieved by performing a proximal spleno-renal shunt. We discuss the likely association of this mesodermal development abnormality and vascular disorders of the portal vein.The American Journal of Gastroenterology 03/1998; 93(2):275-6. · 7.55 Impact Factor
- Cleveland Clinic quarterly 02/1982; 49(4):239-47.