Article

Diagnosis of arrhythmogenic right ventricular dysplasia: a review.

Department of Radiology, Leiden University Medical Center, Albinusdreef 2, 2333 ZA Leiden, The Netherlands.
Radiographics (Impact Factor: 2.73). 05/2002; 22(3):639-48; discussion 649-50. DOI: 10.1148/radiographics.22.3.g02ma07639
Source: PubMed

ABSTRACT Arrhythmogenic right ventricular dysplasia (ARVD) is a myocardial disorder of primarily the right ventricle, with unknown cause and prevalence and with a frequent familial occurrence. The typical clinical manifestation consists of ventricular arrhythmias with a left bundle branch block (LBBB) pattern that occur predominantly in young adults. ARVD may result in sudden death. Other manifestations are electrocardiographic repolarization and depolarization changes, structural abnormalities that range from subtle wall aneurysms within the so-called "triangle of dysplasia" to biventricular regional or global dysfunction, and localized or widespread fibrofatty infiltration of the right ventricular myocardium. The diagnosis of ARVD is based on the presence of major and minor criteria encompassing genetic, electrocardiographic, pathophysiologic, and histopathologic factors. The imaging modalities used to evaluate right ventricular abnormalities include conventional angiography, echocardiography, radionuclide angiography, ultrafast computed tomography, and magnetic resonance (MR) imaging. Among these techniques, MR imaging allows the clearest visualization of the heart. Because MR imaging depicts both functional and structural abnormalities, positive MR imaging findings should be used as important additional criteria in the clinical diagnosis of ARVD. MR imaging appears to be the optimal technique for detection and follow-up of clinically suspected ARVD.

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    ABSTRACT: Right ventricular dysplasia (RVD) is a cardiomyopathy, which is characterized by fatty, or fibro fatty infiltration of myocardium and it is the most common cause of sudden cardiac death in the young. It may be manifested clinically as ventricular arrhythmias with left bundle branch block (LBBB) that may lead to cardiac arrest. So, this condition is also known as Arrhythmogenic right ventricular dysplasia (ARVD).The diagnosis of ARVD is based on the presence of major and minor criteria encompassing genetic, electrocardiographic, pathophysiologic, histopathological factors and imaging modalities. An early and accurate diagnosis followed by appropriate therapy for this condition is increasingly important for it may prevent lethal arrhythmias. Here we are reporting a case of young army man who was died suddenly of RVD along with brief discussion about the Pathophysiology, clinical features, and criteria for diagnosis and differential diagnoses of the condition.
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