Incomplete Kawasaki disease with recurrent skin peeling: a case report with the review of literature.

Department of Paediatric Cardiology, Madras Medical Mission Hospital, 4A, JJ Nagar, Moggapair, Chennai-600 050, India.
Journal of Postgraduate Medicine (Impact Factor: 0.86). 01/2003; 49(1):72-4. DOI: 10.4103/0022-3859.924
Source: PubMed


Kawasaki disease (KD) is an acute systemic vasculitis of unknown aetiology that has largely replaced rheumatic heart disease as a cause of acquired heart disease in children of many developed countries. We report a case of incomplete KD in a five-year-old girl. The diagnosis of incomplete KD was made after exclusion of conditions with similar presentation. She was treated with intravenous immunoglobulin following which she made an uneventful recovery but demonstrated thrombocytosis in the second week of convalescence. During the six-month follow up period, she had two episodes of recurrent skin peeling a phenomenon, which is recently reported with KD but not with atypical or incomplete KD. It is important for the treating physicians to become aware of the incomplete KD as prompt diagnosis and early treatment of these patients with intravenous immunoglobulin is vital for the prevention of lethal coronary complications. Physicians need to have a "high index of suspicion" for KD and even, higher for IKD.

16 Reads
  • Source
    • "et al . , 2007 ) . Although the patient reported here was admitted during the initial episode of her disease and presented with all of the cri - teria of the acute febrile phase , the delayed diagnosis led to the delayed administration of IVIG . This may ultimately have been responsible for the observed late recurrence of the oral manifestations ( Parmar et al . , 2003 ; Pemberton et al . , 1999 ) . Dentists and oral medicine specialists are not usually in - volved in the diagnostic process of Kawasaki disease in chil - dren since the persistent fever tends to be the parents ' main concern . The oral manifestations of the disease are important to recognize since they may be overlooked by the general p"
    [Show abstract] [Hide abstract]
    ABSTRACT: Kawasaki Disease (KD) is an acute systemic vasculitis of unknown etiology. In many developed countries, KD has replaced rheumatic heart disease as the leading cause of acquired heart disease in children. Among the classical criteria for a diagnosis of KD are oral manifestations such as strawberry tongue, erythematous cracked lip, and oropharyngeal mucositis. We report the case of a 24-year-old Saudi female with a history of Kawasaki disease who presented to our oral medicine clinic with recurrent painless swelling of the upper lip. As lip swelling has not previously been reported as an oral manifestation of KD, this case represents a novel presentation of recurrent Kawasaki disease in an adult female.
    Saudi Dental Journal 08/2013; 25(1):43-7. DOI:10.1016/j.sdentj.2012.10.001
  • Source
    [Show abstract] [Hide abstract]
    ABSTRACT: Kawasaki disease is a syndrome of unknown etiology affecting children below 5 years of age and is a leading cause of acquired heart disease in many developed countries. Incidence of this disease in India is extremely low as evidenced by the meagre case reports. Complications due to this disease in Indian patients are still rarer. Here we report two cases of Kawasaki disease both of whom had a benign course. A comparison of this disease in Indian and Western literature shows that the incidence of cardiac complications in the Indian patients is about 10% while in the west it is reported at around 30%. This paucity of complications in the Indian patients may be the reason of poor reporting of this disease in our country.
    The Indian Journal of Pediatrics 09/2001; 68(8):775-7. DOI:10.1007/BF02752421 · 0.87 Impact Factor
  • Source
    [Show abstract] [Hide abstract]
    ABSTRACT: We report 6 cases of Kawasaki disease (KD) diagnosed over a period of one year and review of all the cases reported from India. The diagnosis of KD was based on clinical criteria The mean age of patients was 6.83 years and mean duration of symptoms before diagnosis was 7.5 days. Apart from classical clinical features, elevated transaminases and blood urea along with free fluid in abdomen was present in one case each. Two patients had dilated coronaries that returned to normal on follow up. One patient developed headache and neck stiffness following treatment with intravenous gamma globulins. The outcome was excellent in all the cases.
    The Indian Journal of Pediatrics 11/2005; 72(10):873-5. DOI:10.1007/BF02731119 · 0.87 Impact Factor
Show more